Research Article: 10-Year Clinical Follow-Up after Decompression of Lipofibromatous Hamartoma of the Median Nerve in a 3-Year-Old Patient: Case Report and Review of the Literature
Abstract:
Lipofibromatous hamartoma, first reported in 1953, is a rare, slowly progressive soft tissue tumor, the characteristics of which include the enlargement of the affected nerve via the epineurial and perineurial proliferation of adipose and fibrous tissues. Out of 200 previously reported cases of lipofibromatous hamartoma of the median nerve, there have been approximately 25 pediatric cases under the age of 18. Herein, we report a case of lipofibromatous hamatoma of the median nerve in a 3-year-old female patient who was surgically decompressed via carpal tunnel release and epineurolysis. The patient was followed-up on an outpatient clinic basis annually with sonographic evaluations, and the postoperative 10th-year follow-up did not show recurrence or any deficits in motor and sensory functions.
Introduction:
Lipofibromatous hamartoma (LFH), first reported in 1953, is a rare, slowly progressive, benign soft tissue tumor characterized by the enlargement of the affected nerve by the epineurial and perineurial proliferation of adipose and fibrous tissues [1,2]. While most often found in the upper extremities, the median nerve is the most commonly reported nerve affected by LFH, but there have been previous studies reporting LFH occurring on other nerves, such as the ulnar, radial, and peroneal nerves [2]. Less commonly,…
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